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Rare (<1%) histological subtypes of renal cell carcinoma: an update

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Abstract

Recent advances in genetics and pathology have allowed description of several new histological subtypes of renal cell carcinoma (RCC) as well as better characterization of other rare subtypes. We herein present a comprehensive review of taxonomy, epidemiology, pathology, imaging findings, and natural history of a wide spectrum of rare subtypes of RCCs that individually constitute <1% of all the RCCs.

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Authors and Affiliations

  1. Department of Radiology, University of Texas Health Science Center at San Antonio, 7703 Floyd Curl Drive, San Antonio, TX, 78229, USA

    Alampady K. Shanbhogue

  2. Department of Radiology, M.D. Anderson Cancer Research Center, 1515 Holcombe Boulevard, Houston, TX, 77030, USA

    Raghunandan Vikram

  3. Department of Radiology, University Hospitals, Case Medical Center, Case Western Reserve University, 11100 Euclid Ave, Cleveland, OH, 44106, USA

    Raj Mohan Paspulati

  4. Department of Pathology, University Hospitals, Case Medical Center, Case Western Reserve University, 11100 Euclid Ave, Cleveland, OH, 44106, USA

    Gregory MacLennan

  5. Department of Radiology, University of Cincinnati Medical Center, 234 Goodman Street, Cincinnati, OH, 45267-0761, USA

    Sadhna Verma

  6. Department of Radiology, Indiana University School of Medicine, 340 West 10th Street, Suite 6200, Indianapolis, IN, 46202-3082, USA

    Kumar Sandrasegaran

  7. Department of Radiology, University of Texas M.D. Anderson Cancer Center, 1400 Pressler street, Houston, TX, 77030, USA

    Srinivasa R. Prasad

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  1. Alampady K. Shanbhogue
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  7. Srinivasa R. Prasad
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Correspondence to Srinivasa R. Prasad.

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Shanbhogue, A.K., Vikram, R., Paspulati, R.M. et al. Rare (<1%) histological subtypes of renal cell carcinoma: an update. Abdom Radiol 37, 861–872 (2012). https://doi.org/10.1007/s00261-011-9810-1

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